Gross cerebral atrophy with diffuse paucity of bilateral cerebral white matter is seen causing gross prominence of convexity sulci, sylvian fissures, bilateral lateral and third ventricles.
Diffuse T2/FLAIR hyperintensity is seen in bilateral cerebral white matter.
Diffuse thinning of corpus callosum is seen with partial atrophy of both cerebral peduncles.
Mild atrophy of cerebral is also seen with prominence of fourth ventricle and cerebellar folia.