Features consistent with nephroblastomatosis.

Nephroblastomatosis is a rare condition, considered as a precursor of nephroblastoma (Wilms tumor). It is characterized by the presence of multiple residual embryonal cells (nephrogenic rests). When isolated, the recommended treatment consists of chemotherapy followed by monitoring. In the presence of an associated nephroblastoma, treatment consists of preoperative chemotherapy followed by surgery, then postoperative chemotherapy and monitoring.

Additional contributor: Dr. R Bouguelaa, MD