Granulomatosis with polyangiitis

Discussion:

Patient also had maxillary sinusitis and renal impairment. Findings are consistent with Wegener's granulomatosis (granulomatosis with polyangiitis). Diagnosis was verified.

The classic Wegener's triad represents involvement of upper respiratory tract, lungs and kidneys. Lungs are the most frequently involved site in granulomatosis with polyangiitis (95% of cases). 

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