Herlyn-Werner-Wunderlich syndrome encompasses

• uterine didelphys with vaginal septum causing hemivaginal obstruction
  • consequent unilateral hematocolpos, hematometra, hemosalpix and occasionally hemoperitoneum
• contralateral Mullerian duct is well developed so that the patient presentation is often vague as there is no amenorrhea.
• ipsilateral renal agenesis with compensatory hypertrophy of the contralateral kidney

This patient underwent resection of the left hemiuterus with improvement of her symptoms.