Congenital aortic stenosis
Updates to Article Attributes
A congenitalCongenital aortic stenosis broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often refersrelates to a narrowing aboutof the aortic valve. As a broad group, there can be some overlap with ascending aortic coarctation depending ofon the definition used.
Pathology
Depending on location it can be classified into 3three types.:
-
supravalvularsupra valvular stenosis - congenital aortic valve stenosis (commonest)
- subvalvular stenosis
Associations
-
Williams syndrome: with
supravalvularsupra valvular type - bicuspid aortic valve 2,4
- aortic coarctation
- hypoplastic left heart
- quadricuspid aortic valve 4
Radiographic features
Plain radiograph
Chest radiographs can be normal or may show evidence of cardiomegaly.
Echocardiography
May show a high flow jet through the aortic valve or narrowed segment.
CT / MRI
Apart from showing a narrowed valve annulus and/or narrowing cross sectional-sectional aortic segment it may also show:
- cardiomegaly with left ventricular hypertrophy
- post
stenotic-stenotic dilated segment of the aortic lumen
In MR imaging, velocity encoded phase contrast cine sequences can assist assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes 2
Doppler ultrasound / echocardiography
May show a high flow jet through the aortic valve or narrowed segment
See also
-<p>A <strong>congenital aortic stenosis</strong> broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point it often refers to a narrowing about the <a href="/articles/aortic-valve">aortic valve</a>. As a broad group there can be some overlap with ascending <a href="/articles/coarctation-of-the-aorta">aortic coarctation</a> depending of the definition used. </p><p>Depending on location it can be classified into 3 types.</p><ol>-<li>supravalvular stenosis</li>- +<p><strong>Congenital aortic stenosis</strong> broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often relates to a narrowing of the <a href="/articles/aortic-valve">aortic valve</a>. As a broad group, there can be some overlap with ascending <a href="/articles/coarctation-of-the-aorta">aortic coarctation</a> depending on the definition used. </p><h4>Pathology</h4><p>Depending on location it can be classified into three types:</p><ul>
- +<li>supra valvular stenosis</li>
-</ol><h5>Associations</h5><ul>-<li>-<a href="/articles/williams-syndrome">Williams syndrome</a> : with supravalvular type</li>- +</ul><h5>Associations</h5><ul>
- +<li>Williams syndrome: with supra valvular type</li>
-</ul><h4>Radiographic features</h4><h5>Plain radiograph</h5><p>Chest radiographs can be normal or may show evidence of cardiomegaly.</p><h5>CT / MRI</h5><p>Apart from showing a narrowed valve annulus and/or narrowing cross sectional aortic segment it may also show </p><ul>- +</ul><h4>Radiographic features</h4><h5>Plain radiograph</h5><p>Chest radiographs can be normal or may show evidence of cardiomegaly.</p><h5>Echocardiography</h5><p>May show a high flow jet through the aortic valve or narrowed segment.</p><h5>CT / MRI</h5><p>Apart from showing a narrowed valve annulus and/or narrowing cross-sectional aortic segment it may also show:</p><ul>
-<li>post stenotic dilated segment of the aortic lumen</li>-</ul><p>In MR imaging, velocity encoded phase contrast cine sequences can assist assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes <sup>2</sup></p><h5><strong>Doppler ultrasound / echocardiography</strong></h5><p>May show a high flow jet through the aortic valve or narrowed segment</p><h4>See also </h4><ul>- +<li>post-stenotic dilated segment of the aortic lumen</li>
- +</ul><p>In MR imaging, velocity encoded phase contrast cine sequences can assist assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes <sup>2</sup></p><h4>See also </h4><ul>
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