Congenital utero-vaginal anomalies

Changed by Craig Hacking, 8 Mar 2016

Updates to Article Attributes

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There are many classification systems for congenital utero-vaginal anomalies. These include

  • Buttram and Gibbons classification 2
  • American Fertility Society (AFS) classification
  • modified Rock and Adam - AFS classification
Modified Rock and Adam - AFS classification

This classification divides congenital uterine anomalies into four main types:

  • class I - dysgenesis ofMüllerian ducts
    • includes agenesis or hypoplasia of themüllerian duct derivatives: the uterus andupper two-thirds of the vagina
    • the most commonform is the Mayer-Rokitansky-Kuster-Hauser syndrome - is combinedagenesisof the uterus, cervix, and upper portion of thevagina
  • class II - disorders of vertical fusion
    • these anomalies are due to failure of fusion of the müllerian system with the sinovaginal bulb
    • they include cervical dysgenesis and obstructive and nonobstructive transverse vaginal septa
  • class III- disorders of lateralfusion
    • describes anomalies that result in a duplicated orpartially duplicated reproductivetract
    • these disorders are due to impaired fusionand / or septal resorption of fusing Müllerian ducts attempting to formtheuterus, cervix, and upper vagina
    • it includesanomalies due to failure of fusion of the paired müllerian ducts (as in didelphicand bicornuate uteri) and failure of midlineseptum resorption after fusion (as in septate uterus)
    • disorders due tolateralfusion defects are further subclassified into 
      • a- symmetric non-obstructive forms seen in five types: unicornuate, bicornuate, didelphic, septate, and DES-related uteri
      • b - asymmetric obstructive forms seen in three types: unicornuate uterus with obstructed horn, double uterus with unilaterallyobstructed horn, and double uterus with unilaterally obstructed vagina
  • class IV - unusual configurations and combinations of defects
  • -</li>
  • -<li>American Fertility Society (AFS) classification</li>
  • -<li>modified Rock and Adam - AFS classification</li>
  • +</li>
  • +<li>American Fertility Society (AFS) classification</li>
  • +<li>modified Rock and Adam - AFS classification</li>
  • -<li>
  • -<strong>class I</strong> - dysgenesis of
  • -Müllerian ducts<ul>
  • -<li>includes agenesis or hypoplasia of the
  • -müllerian duct derivatives: the uterus and
  • - upper two-thirds of the vagina</li>
  • -<li>the most common
  • -form is the <a href="/articles/mayer-rokitansky-kuster-hauser-syndrome" title="Mayer-Rokitansky-Küster-Hauser syndrome">Mayer-Rokitansky-Kuster-Hauser syndrome</a> - is combined
  • -agenesis
  • - of the uterus, cervix, and upper portion of the
  • -vagina</li>
  • +<li>
  • +<strong>class I</strong> - dysgenesis of Müllerian ducts<ul>
  • +<li>includes agenesis or hypoplasia of the müllerian duct derivatives: the uterus and upper two-thirds of the vagina</li>
  • +<li>the most common form is the <a href="/articles/mayer-rokitansky-kuster-hauser-syndrome">Mayer-Rokitansky-Kuster-Hauser syndrome</a> - is combined agenesis of the uterus, cervix, and upper portion of the vagina</li>
  • -</li>
  • -<li>
  • +</li>
  • +<li>
  • -<li>these anomalies are due to failure of fusion of the müllerian system with the sinovaginal bulb</li>
  • -<li>they include cervical dysgenesis and obstructive and nonobstructive <a href="/articles/transverse-vaginal-septa" title="transverse vaginal septa">transverse vaginal septa</a>
  • -</li>
  • +<li>these anomalies are due to failure of fusion of the müllerian system with the sinovaginal bulb</li>
  • +<li>they include cervical dysgenesis and obstructive and nonobstructive <a href="/articles/transverse-vaginal-septa">transverse vaginal septa</a>
  • +</li>
  • -</li>
  • -<li>
  • -<strong>class III </strong>- disorders of lateral
  • - fusion<ul>
  • -<li>describes anomalies that result in a duplicated or
  • -partially duplicated reproductive
  • - tract</li>
  • -<li>these disorders are due to impaired fusion
  • -and / or septal resorption of fusing Müllerian ducts attempting to form
  • -the
  • - uterus, cervix, and upper vagina</li>
  • -<li>it includes
  • -anomalies due to failure of fusion of the paired müllerian ducts (as in
  • -<a href="/articles/uterus_didelphys" title="Didelphic uterus">didelphic</a>
  • - and <a href="/articles/bicornuate_uterus" title="Bicornuate uterus">bicornuate</a> uteri) and failure of midline
  • -septum resorption after fusion (as in <a href="/articles/septate-uterus" title="Septate uterus">septate uterus</a>)</li>
  • -<li>disorders due to
  • -lateral
  • - fusion defects are further subclassified into <ul>
  • -<li>
  • -<strong>a </strong>- symmetric <strong>non-obstructive forms</strong> seen in five types: unicornuate, bicornuate, didelphic, septate, and DES-related uteri</li>
  • -<li>
  • -<strong>b</strong> - asymmetric <strong>obstructive forms</strong> seen in three types: unicornuate uterus with obstructed horn, double uterus with unilaterally
  • - obstructed horn, and double uterus with unilaterally obstructed vagina</li>
  • +</li>
  • +<li>
  • +<strong>class III </strong>- disorders of lateral fusion<ul>
  • +<li>describes anomalies that result in a duplicated or partially duplicated reproductive tract</li>
  • +<li>these disorders are due to impaired fusion and / or septal resorption of fusing Müllerian ducts attempting to form the uterus, cervix, and upper vagina</li>
  • +<li>it includes anomalies due to failure of fusion of the paired müllerian ducts (as in <a href="/articles/uterus-didelphys">didelphic</a> and <a href="/articles/bicornuate-uterus">bicornuate</a> uteri) and failure of midline septum resorption after fusion (as in <a href="/articles/septate-uterus">septate uterus</a>)</li>
  • +<li>disorders due to lateral fusion defects are further subclassified into <ul>
  • +<li>
  • +<strong>a </strong>- symmetric <strong>non-obstructive forms</strong> seen in five types: unicornuate, bicornuate, didelphic, septate, and DES-related uteri</li>
  • +<li>
  • +<strong>b</strong> - asymmetric <strong>obstructive forms</strong> seen in three types: unicornuate uterus with obstructed horn, double uterus with unilaterally obstructed horn, and double uterus with unilaterally obstructed vagina</li>
  • -</li>
  • +</li>
  • -</li>
  • -<li>
  • -<strong>class IV</strong> - unusual configurations and combinations of defects</li>
  • +</li>
  • +<li>
  • +<strong>class IV</strong> - unusual configurations and combinations of defects</li>
Images Changes:

Image 1 CT (C+ portal venous phase) ( create )

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