Cyanotic congenital heart disease

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A number of entities can present as cyanotic congenital heart disease. These can be divided into those with increased (pulmonary plethora) or decreased pulmonary vascularity :

increased pulmonary vascularity
- total anomalous pulmonary venous return (TAPVR) (types I and II)
- transposition of the great arteries (TGA)
- truncus arteriosus (types I, II and III)
- large AVSD
- single ventricle without pulmonary stenosis
decreased pulmonary vascularity
- tetralogy of Fallot
- hypoplastic right heart syndrome: pulmonary vascularity dependent on systemic collaterals
  - tricuspid atresia
  - hypoplastic right ventricle
  - pulmonary atresia or severe stenosis
- Ebstein anomaly with atrial septal defect
- many other combined and infrequent anomalies such as
  - double outlet right ventricle (DORV) with pulmonary stenosis
  - single ventricle with pulmonary stenosis
  - ~~Ebstein anomaly~~ ~~with~~ ~~atrial septal defect~~
  - Uhl anomaly
  - pentalogy of Cantrell

The most important cyanotic congenital heart defects can be remembered with the five T's mnemonic.

~~-<li><a href="/articles/pentalogy-of-cantrell-3">pentalogy of Cantrell</a></li>~~
~~-<li>many other combined and infrequent anomalies such as<ul>~~
~~-<a href="/articles/double-outlet-right-ventricle">double outlet right ventricle (DORV) </a>with pulmonary stenosis</li>~~
~~-<li>single ventricle with pulmonary stenosis</li>~~
+<a title="Hypoplastic right heart syndrome" href="/articles/hypoplastic-right-heart-syndrome">hypoplastic right heart syndrome</a>: pulmonary vascularity dependent on systemic collaterals<ul>
+<li><a title="Tricuspid atresia" href="/articles/tricuspid-atresia">tricuspid atresia</a></li>
+<li>hypoplastic right ventricle</li>
+<li>
+<a title="Pulmonary atresia" href="/articles/pulmonary-artery-atresia">pulmonary atresia</a> or severe stenosis</li>
+</ul>
+</li>
+<li>many other combined and infrequent anomalies such as<ul>
+<li>
+<a href="/articles/double-outlet-right-ventricle">double outlet right ventricle (DORV) </a>with pulmonary stenosis</li>
+<li>single ventricle with pulmonary stenosis</li>
+<li><a href="/articles/pentalogy-of-cantrell-3">pentalogy of Cantrell</a></li>
~~-</ul>~~
+</ul><p>The most important cyanotic congenital heart defects can be remembered with the <a title="The five T's of cyanotic congenital heart disease (mnemonic)" href="/articles/the-five-ts-of-cyanotic-congenital-heart-disease-mnemonic">five T's</a> mnemonic.</p>