Question 1787
{"accessible":true,"alternatives":[{"id":8876,"text":"Adult polycystic kidney disease"},{"id":8877,"text":"Fabry disease"},{"id":8878,"text":"Hereditary hemorrhagic telangiectasia"},{"id":8879,"text":"Neurofibromatosis type 1"},{"id":8880,"text":"Sturge-Weber syndrome"}],"archived":false,"correctAlternativeId":8877,"explanation":"\u003cp\u003e\u003ca href=\"/articles/fabry-disease\" title=\"Fabry disease\"\u003eFabry disease\u003c/a\u003e\u0026nbsp;is a multisystem disorder resulting from an X-linked inborn error of metabolism and is a lysosomal storage disorder.\u0026nbsp;Renal involvement begins with proteinuria progressing to end-stage renal failure, usually in the 4th decade.\u0026nbsp;\u003c/p\u003e\u003cp\u003eSmall vessel ischemia is the main mechanism of central nervous system manifestations, with ischemic strokes, especially of the posterior circulation being common.\u0026nbsp;Additionally, basilar artery \u003ca href=\"/articles/dolichoectasia-1\" title=\"Dolichoectasia\"\u003edolichoectasia\u003c/a\u003e is characteristic of this disease.\u0026nbsp;\u003c/p\u003e","id":1787,"imageUrl":"https://prod-images-static.radiopaedia.org/multiple_choice_questions/279/FG_MCQ_my_copy__WIDE_.key_big_gallery.jpeg","imageAttribution":{"kind":"external","attribution":"Dr Budzko rID: 31495 (this case is not actually of Fabry disease) "},"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/2591","nextQuestionPath":"/articles/ischaemic-stroke/questions/1748","relatedArticles":[{"id":5026,"title":"Dolichoectasia","link":"/articles/dolichoectasia-1?lang=us"},{"id":37570,"title":"End-stage renal disease","link":"/articles/end-stage-renal-disease-2?lang=us"}],"alsoUsedIn":[{"id":771,"kind":"Course","title":"Stroke Learning Pathway - page 771","link":"https://radiopaedia.org/courses/stroke-learning-pathway/pages/771"},{"id":2108,"kind":"Course","title":"Stroke Learning Pathway - peer review - page 2108","link":"https://radiopaedia.org/courses/stroke-learning-pathway-peer-review/pages/2108"}],"stem":"\u003cp\u003eA 40-year-old man with end-stage renal failure suffers acute features consistent with a\u0026nbsp;pontine infarct. A\u0026nbsp;CT demonstrates the following features. What is the most likely underlying condition?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/1787"}],"attemptsPercentages":[{"alternativeId":"8878","percentage":17},{"alternativeId":"8876","percentage":41},{"alternativeId":"8877","percentage":23},{"alternativeId":"8880","percentage":11},{"alternativeId":"8879","percentage":7}],"promptToLogin":false,"questionManager":false,"articleId":"ischemic-stroke"}