Pediatric cystic renal diseases
Updates to Article Attributes
Body
was changed:
The paediatric cystic renal diseases comprises a group of conditions that are all either autosomal recessive or non-hereditary:
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autosomal recessive polycystic kidney disease (ARPKD):
- hyperechoic and enlarged kidney
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multicystic dysplastic kidney (MCDK):
- absence of functional parenchyma, ureteral and arterial atresia
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mulitlocular cystic nephroma (MLCN):
- multiple very large cysts
nephronophthosisnephronophthisis - medullary cystic disease complex
Differential diagnosis
- cystic Wilms tumor
-<li>- +<li>
-</li>-<li>-<a href="/articles/multicystic-dysplastic-kidney" title="Multicystic dysplastic kidney (MCDK)">multicystic dysplastic kidney (MCDK)</a>:<ul><li>absence of functional parenchyma, ureteral and arterial atresia</li></ul>-</li>-<li>- +</li>
- +<li>
- +<a href="/articles/multicystic-dysplastic-kidney">multicystic dysplastic kidney (MCDK)</a>:<ul><li>absence of functional parenchyma, ureteral and arterial atresia</li></ul>
- +</li>
- +<li>
-</li>-<li><a href="/articles/medullary-cystic-disease-complex">nephronophthosis - medullary cystic disease complex</a></li>-</ul><h4>Differential diagnosis</h4><ul><li>cystic <a href="/articles/wilms-tumour" title="Wilms tumors">Wilms tumor</a>- +</li>
- +<li><a href="/articles/medullary-cystic-disease-complex">nephronophthisis - medullary cystic disease complex</a></li>
- +</ul><h4>Differential diagnosis</h4><ul><li>cystic <a href="/articles/wilms-tumour">Wilms tumor</a>