Primary intracranial leiomyosarcoma
Updates to Article Attributes
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Primary intracranial leiomyosarcomas are primary malignant tumours derived from smooth muscle cell lineage in the cranial vault.
Epidemiology
Primary intracranial leiomyosarcomas are extremely rare. Most commonly, these lesions have been described as EBV associated smooth muscle tumours in patients who are immunocompromised due to HIV infection.
Radiographic features
Intracranial leiomyosarcoma usually appears as an extra-axial mass 1,2, with intra-axial mass being a rare presentation 3,4.
MRI
The signal characteristics are nonspecific 4.
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T1
- isointense to hypointense
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T2
- variable
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T1 C+
- vividly enhancing and heterogeneous
See also
-<p><strong>Primary intracranial leiomyosarcomas </strong>are primary malignant tumours derived from smooth muscle cell lineage in the cranial vault.</p><h4>Epidemiology</h4><p>Primary intracranial leiomyosarcomas are extremely rare. Most commonly, these lesions have been described as <a title="EBV associated smooth muscle tumour" href="/articles/ebv-associated-smooth-muscle-tumour">EBV associated smooth muscle tumours</a> in patients who are immunocompromised due to <a title="HIV associated neoplasms" href="/articles/hiv-associated-neoplasms">HIV</a> infection.</p><h4>Radiographic features</h4><p>Intracranial leiomyosarcoma usually appears as an extra-axial mass <sup>1,2</sup>, with intra-axial mass being a rare presentation <sup>3,4</sup>.</p><h5>MRI</h5><p>The signal characteristics are nonspecific <sup>4</sup>.</p><ul>- +<p><strong>Primary intracranial leiomyosarcomas </strong>are primary malignant tumours derived from smooth muscle cell lineage in the cranial vault.</p><h4>Epidemiology</h4><p>Primary intracranial leiomyosarcomas are extremely rare. Most commonly, these lesions have been described as <a href="/articles/ebv-associated-smooth-muscle-tumour">EBV associated smooth muscle tumours</a> in patients who are immunocompromised due to <a href="/articles/hiv-associated-neoplasms">HIV</a> infection.</p><h4>Radiographic features</h4><p>Intracranial leiomyosarcoma usually appears as an extra-axial mass <sup>1,2</sup>, with intra-axial mass being a rare presentation <sup>3,4</sup>.</p><h5>MRI</h5><p>The signal characteristics are nonspecific <sup>4</sup>.</p><ul>
-</ul><h4>See also</h4><ul><li><a title="Leiomyosarcoma" href="/articles/leiomyosarcoma">leiomyosarcoma</a></li></ul>- +</ul><h4>See also</h4><ul><li><a href="/articles/leiomyosarcoma">leiomyosarcoma</a></li></ul>
Images Changes:
Image 1 MRI (T1 C+) ( update )
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