Pulmonary vasculitis
Updates to Article Attributes
Pulmonary vasculitis refers to vasculitides that affect the lung that affects the lung/pulmonary/ pulmonary vessels. If this definition is used, a large group of conditions can fall into this category.
The The respiratory system may be potentially involved in all systemic vasculitides, although to a variable degree4
Pathology
When using the term "vasculitis", this implies that an inflammatory component is present within the pulmonary vessels.
Various classification systems have been published including popular Chapel Hill consensus classification system 7.
Small vessel vasculitides
The group that classically forms a dominantthe dominant pulmonary vasculitis tends to include the small vessel inflammatory processes that affect the pulmonary vessels.These include:
- ANCA associated vasculitides
- idiopathic, pauci-immune pulmonary capillaritis (IPIPC): may or may not be ANCA associated
- non ANCA associated pulmonary renal syndrome: Goodpasture syndrome 2
- rheumatoid pulmonary vasculitis 8: rare
Large vessel vasculitides
The former three can also frequently have extra-pulmonary manifestations.
According to some authors, largeLarge vessel vasculitides arecan also included in this group,affect the lung and these includepulmonary vessels:
- Takayasu arteritis: 50-80% pulmonary involvement 1
- giant cell arteritis
- Behçet disease: 1-8% thoracic involvement 1
- Hugh Stovin syndrome
Granulomatous disease
In addition certain granulomatous processes in the lung can also have an angiocentric component. Such include 3:
Classification
Various classification systems have been published including popular Chapel Hill consensus classification system7.
-<p><strong>Pulmonary vasculitis</strong> refers a <a href="/articles/vasculitis">vasculitis</a> that affects the lung/pulmonary vessels. If this definition is used, a large group of conditions can fall into this category. </p><p>The respiratory system may be potentially involved in all systemic vasculitides, although to a variable degree <sup>4</sup>. </p><p>When using the term "vasculitis", this implies that an inflammatory component is present within the pulmonary vessels.</p><p>Various classification systems have been published including popular Chapel Hill consensus classification system <sup>7</sup>.</p><p>The group that classically forms a dominant pulmonary vasculitis tends to include the small vessel inflammatory processes that affect the pulmonary vessels.These include:</p><ul>- +<p><strong>Pulmonary vasculitis</strong> refers to vasculitides that affect the <a title="Lung anatomy" href="/articles/lung">lung</a> / pulmonary vessels. If this definition is used, a large group of conditions can fall into this category. The respiratory system may be potentially involved in all systemic vasculitides, although to a variable degree. </p><h4>Pathology</h4><p>When using the term "vasculitis", this implies that an inflammatory component is present within the pulmonary vessels.</p><h5>Small vessel vasculitides</h5><p>The group that classically forms the dominant pulmonary vasculitis tends to include the small vessel inflammatory processes that affect the pulmonary vessels:</p><ul>
-</ul><p>The former three can also frequently have extra-pulmonary manifestations. </p><p>According to some authors, <a href="/articles/large-vessel-vasculitides">large vessel vasculitides</a> are also included in this group, and these include:</p><ul>- +</ul><h5>Large vessel vasculitides</h5><p><a href="/articles/large-vessel-vasculitides">Large vessel vasculitides</a> can also affect the lung and pulmonary vessels:</p><ul>
-</ul><p>In addition certain granulomatous processes in the lung can also have an angiocentric component. Such include <sup>3</sup>:</p><ul>- +</ul><h5>Granulomatous disease</h5><p>In addition certain granulomatous processes in the lung can also have an angiocentric component <sup>3</sup>:</p><ul>
-</ul>- +</ul><h5>Classification</h5><p>Various classification systems have been published including popular <a title="Chapel Hill consensus classification system" href="/articles/chapel-hill-consensus-classification-system">Chapel Hill consensus classification system</a> <sup>7</sup>.</p>
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