Presentation
Ataxia
Patient Data
Predominantly nonenhancing hypodense mass in the right cerebellum causing mass effect on the posterior fossa structures, with effacement of the 4th ventricle.
MRI demonstrates a T1 hypointense T2 hyperintense nonenhancing lesion in the right cerebellum. T2-characteristics are classic, and show widened cerebellar folia with striated, "corduroy" appearance. The mass causes mass effect on the posterior fossa structures and effaces the 4th ventricle. There is no associated restricted diffusion nor increased perfusion.
Case Discussion
Lhermitte-Duclos (dysplastic gangliocytoma of the cerebellum) is a rare hamartomatous tumor of the cerebellum. It usually presents in young adults and is associated with Cowden's disease. MRI appearance is classic, with striated, "corduroy" appearance of widened cerebellar folia.
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