Endolymphatic sac tumor
Diagnosis certain
Disclosures
- updated 18 Aug 2022:
Nothing to disclose
Updates to Study Attributes
Caption
was changed:
MRI study of abdome that shows another vHL common feature: multiple renal cystsAbdomen (selected images)
Updates to Case Attributes
Body
was changed:
Patient with von Hippel-Lindau syndrome (vHL) and had previously resected a left cerebellar hemangioblastomahaemangioblastoma (signs of cranioplasty on CT).
These studies show a mass in retro labyrinthine portion of the right temporal bone, involving part of jugular foramen, that was confirmed as an endolymphatic sac tumour, which occurs in about 16% of patients with von Hippel-Lindau syndrome.
This patient also has an MRI study of the abdomen showing another vHL feature: multiple renal cysts.
-<p>Patient with <a href="/articles/von-hippel-lindau-disease-5">von Hippel-Lindau syndrome (vHL)</a> and had previously resected a left <a href="/articles/haemangioblastoma-central-nervous-system-1">cerebellar hemangioblastoma</a> (signs of cranioplasty on CT).</p><p>These studies show a mass in retro labyrinthine portion of the right temporal bone, involving part of jugular foramen, that was confirmed as an <a href="/articles/endolymphatic-sac-tumour">endolymphatic sac tumour</a>, which occurs in about 16% of patients with von Hippel-Lindau syndrome.</p><p>This patient also has an MRI study of the abdomen showing another vHL feature: multiple renal cysts.</p>- +<p>Patient with <a href="/articles/von-hippel-lindau-disease-5">von Hippel-Lindau syndrome (vHL)</a> and had previously resected a left <a href="/articles/haemangioblastoma-central-nervous-system-1">cerebellar haemangioblastoma</a> (signs of cranioplasty on CT).</p><p>These studies show a mass in retro labyrinthine portion of the right temporal bone, involving part of jugular foramen, that was confirmed as an <a href="/articles/endolymphatic-sac-tumour">endolymphatic sac tumour</a>, which occurs in about 16% of patients with von Hippel-Lindau syndrome.</p><p>This patient also has an MRI study of the abdomen showing another vHL feature: multiple renal cysts.</p>
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