Kaposiform hemangioendothelioma
Updates to Case Attributes
Kaposiform haemangioendothelioma (KHE) is a rare vascular tumor, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with infantile haemangioma due to the age of presentation and presence of a vascular cutaneous lesion.
KHE tends to proliferate over several months followed by slow involution over many years.
KHE is an infiltrative tumortumour that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.
T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.
Kasabach-Merritt phenomenon (KMP) is profound thrombocytopaeniathrombocytopenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital hemangiomahaemangioma.
-<p>Kaposiform haemangioendothelioma (KHE) is a rare vascular tumor, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with infantile haemangioma due to the age of presentation and presence of a vascular cutaneous lesion.</p><p>KHE tends to proliferate over several months followed by slow involution over many years.</p><p>KHE is an infiltrative tumor that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.</p><p>T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.</p><p>Kasabach-Merritt phenomenon (KMP) is profound thrombocytopaenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital hemangioma.</p>- +<p>Kaposiform haemangioendothelioma (KHE) is a rare vascular tumor, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with infantile haemangioma due to the age of presentation and presence of a vascular cutaneous lesion.</p><p>KHE tends to proliferate over several months followed by slow involution over many years.</p><p>KHE is an infiltrative tumour that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.</p><p>T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.</p><p>Kasabach-Merritt phenomenon (KMP) is profound thrombocytopenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital haemangioma.</p>
Updates to Study Attributes
MRI of the left lower limb shows extensive unilateral limb overgrowth with ill defined-defined thickening involving multiple tissue planes. There is thickening and hyperenhancmenthyperenhancement of the skin with marked enlargement and reticular stranding of the subcutis. Abnormal signal and thickening are also noted in the anterior thigh musculatauremusculature. Large dilated veins are seen in the calf.
Unable to process the form. Check for errors and try again.