Kaposiform hemangioendothelioma
Updates to Case Attributes
Kaposiform haemangioendothelioma (KHE) is a rare vascular tumortumour, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with infantile haemangioma due to the age of presentation and presence of a vascular cutaneous lesion.
KHE tends to proliferate over several months followed by slow involution over many years.
KHE is an infiltrative tumour that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.
T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.
Kasabach-Merritt phenomenon (KMP) is profound thrombocytopenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital haemangioma.
-<p>Kaposiform haemangioendothelioma (KHE) is a rare vascular tumor, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with infantile haemangioma due to the age of presentation and presence of a vascular cutaneous lesion.</p><p>KHE tends to proliferate over several months followed by slow involution over many years.</p><p>KHE is an infiltrative tumour that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.</p><p>T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.</p><p>Kasabach-Merritt phenomenon (KMP) is profound thrombocytopenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital haemangioma.</p>- +<p><a href="/articles/kaposiform-haemangioendothelioma" title="Kaposiform hemangioendothelioma">Kaposiform haemangioendothelioma (KHE)</a> is a rare vascular tumour, typically presenting in infancy as a distinctive cutaneous lesion with ill-defined borders. KHE can be confused with <a href="/articles/infantile-haemangioma" title="Infantile hemangioma">infantile haemangioma</a> due to the age of presentation and presence of a vascular cutaneous lesion.</p><p>KHE tends to proliferate over several months followed by slow involution over many years.</p><p>KHE is an infiltrative tumour that has a tendency to cross tissue planes involving dermis, subcutis, fascia, muscle and bone.</p><p>T1 weighted imaging reveals characteristic, ill-defined hypointense soft tissue thickening involving multiple planes. T2 typically demonstrates hyperintense masses with reticular stranding in the subcutaneous fat.</p><p><a href="/articles/kasabach-merritt-syndrome-1" title="Kasabach-Merritt syndrome">Kasabach-Merritt phenomenon (KMP)</a> is profound thrombocytopenia which results from intralesional platelet trapping. KMP occurs with KHE and tufted angioma but not infantile or congenital haemangioma.</p>
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