Scimitar syndrome

Case contributed by Maxime St-Amant , 8 Dec 2012
Diagnosis certain
Changed by Mostafa Elfeky, 2 Dec 2019

Updates to Case Attributes

Age changed from 60 to 60 years .
Body was changed:

Scimitar syndrome is also known as hypogenetic lung syndrome with four features (but not all four are always present):

  • lung hypoplasia
  • hypoplasia of ipsilateral pulmonary artery
  • anamolousanomalous venous return
  • anamolousanomalous arterial supply
  • -<li>anamolous venous return</li>
  • -<li>anamolous arterial supply</li>
  • +<li>anomalous venous return</li>
  • +<li>anomalous arterial supply</li>

Updates to Study Attributes

Caption was added:
Chest
Findings was changed:

The right hemithorax is hypoplastic. Also, a tubular structure is seen in the lower right lung, which has the shape of a scimitar; the findings are suggestive of Scimitar's syndrome (pulmonary venolobar syndrome or hypogenetic lung syndrome), a type of partial anomalous pulmonary venous return (PAPVR). The heart is displaced to the right. The left pulmonary artery is very prominent.

Images Changes:

Image X-ray (Frontal) ( update )

Description was removed:
Abnormal curvilnear shadow overlying the heart in the right hemithorax - characteristic Scimitar finding.

Updates to Study Attributes

Caption was added:
Chest

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