Chiari 1.5 malformation with syrinx

Case contributed by Ammar Haouimi
Diagnosis almost certain

Presentation

Intermittent neck pain with vertigo.

Patient Data

Age: 40 years
Gender: Male

The MRI sequences demonstrate:

  • caudal descent of the cerebellar tonsils through the foramen magnum, located 12 mm below the McRae line on sagittal sequences

  • associated caudal herniation of the medulla oblongata

  • associated syrinx of the cervical cord at C6-7 level

  • central disc protrusion at C5-6 and C6-7 levels

Case Discussion

MRI features of Chiari 1.5 malformation with syrinx of the cervical spinal cord.

Chiari 1.5 malformation is defined as a combination of cerebellar tonsillar herniation (as seen in Chiari I malformation) along with caudal herniation of some portion of the brainstem (often obex of the medulla oblongata) through the foramen magnum. It is considered a progression of Chiari I malformation.

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