Presentation
Cyanosis since birth
Patient Data
Age: 1 year
Gender: Male
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- mesocardia
- morphologic right ventricle on the right and morphologic left ventricle on the left
- left atrial isomerism with atrial septal defect
- right pulmonary veins drain into the right-sided atrium
- left pulmonary veins, left superior vena cava and left suprahepatic inferior vena cava drain into the left-sided atrium
- double outlet right ventricle with subpulmonic ventricular septal defect (Taussig-Bing anomaly)
- right-sided aorta
- left-sided suprahepatic inferior vena cava and right-sided infrahepatic inferior vena cava
- bilateral hyparterial bronchi
- midline liver
- polysplenia
- left-sided stomach
Case Discussion
This is a case of heterotaxy syndrome with complex congenital heart disease.