Presentation
Omphalocele - follow-up study.
Patient Data
The right liver lobe appears partially malrotated, with its inferior edge cranially pointing superolaterally towards the right hypochondriac fossa. The inferior vena cava and the hepatic veins show concordant clockwise malrotation and are not dilated. Normal liver span of 4.8 cm. The spleen, pancreas, and both kidneys are orthotopic and maintain their normal sizes, shapes, and echotextures.
The heart is well visualized, with a leftward pointing apex, with subtle displacement to the left mediastinum.
Case Discussion
A neonate on management for omphalocele is subjected to routine abdominal, kidney, ureter, and bladder (KUB) ultrasound screening, which in this case revealed partial in-situ malrotation of the right liver lobe, albeit with no organomegaly or focal lesions. Isolated, total, or partial liver malrotation is extremely rare, with very few cases reported in the literature 1-3. In this case, the partial in-situ malrotation is primarily attributed to the congenital omphalocele.
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